MediAI

 Edited by ScholarGen MediAI Team When One Kidney Is Missing, Look Beyond the Kidney Executive Clinical Summary A man in his early 60s underwent CT urography for gross hematuria. The primary clinical question was the source of the bleeding, but the examination revealed an unexpected congenital genitourinary anomaly. The left kidney was normally formed, whereas the right renal parenchyma was not identified. The right renal artery and vein were also absent. The right adrenal gland appeared elongated and flattened rather than normally triangular, and the right seminal vesicle was not clearly visualized. Taken together, these findings support congenital unilateral renal-seminal vesicle agenesis . The diagnostic lesson is broader than the diagnosis itself. An absent kidney on CT should never automatically be labeled renal agenesis. The radiologist should determine whether the missing kidney is truly absent, severely atrophic, ectopic, or surgically absent. The renal vessels, ipsilateral...

Herlyn-Werner-Wunderlich Syndrome: A Rare Triad of Müllerian and Renal Anomaly Herlyn-Werner-Wunderlich (HWW) syndrome, also referred to as Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA), is a rare congenital disorder characterized by a unique triad: uterine didelphys (complete duplication of the uterus and cervix), obstructed hemivagina (often presenting as hematocolpos), and ipsilateral renal agenesis. Though rare, timely diagnosis is crucial to prevent long-term complications like endometriosis, infertility, and infection. 1. Etiology and Pathogenesis Herlyn-Werner-Wunderlich syndrome results from abnormal development and fusion of the Müllerian (paramesonephric) ducts during embryogenesis. Normally, these ducts fuse in the midline to form the uterus, cervix, and upper two-thirds of the vagina, while the Wolffian (mesonephric) ducts contribute to kidney and ureteral development. In HWW syndrome: One Müllerian duct fails to fuse or canalize properly. A longitudinal...