Restrictive Allograft Syndrome (RAS) as a Form of Restrictive Chronic Lung Allograft Dysfunction (rCLAD) with a Pleuroparenchymal Fibroelastosis (PPFE) CT Pattern: A Case-Based Review
Restrictive Allograft Syndrome (RAS) as a Form of Restrictive Chronic Lung Allograft Dysfunction (rCLAD) with a Pleuroparenchymal Fibroelastosis (PPFE) CT Pattern: A Case-Based Review Case Presentation A 46-year-old woman with a prior history of lung cancer and right upper lobectomy presented with progressive abdominal distension, bilateral lower extremity edema, and exertional dyspnea over several months. Initial Chest CT Findings with IV Contrast: [Figure 1] Axial C+ – Demonstrates a markedly enlarged right atrium bulging into the left atrium, consistent with an atrial septal aneurysm . [Figure 2] Axial C+ – Flattening of the interventricular septum with an increased right ventricle to left ventricle ratio, indicating elevated RV pressure. [Figure 3] Axial C+ – Contrast reflux deep into the hepatic veins. The main pulmonary artery is dilated to approximately 3.5 cm, a common finding in pulmonary hypertension . Quiz 1 Q1. Which diagnosis ...